Figur 1. Schematisk beskrivning av binjurebarkens steroidsyntes.

17OH5P = 17a-hydroxi-5-pregnenolon
17OHP = 17a -hydroxiprogesteron
17,21-diOHP = 17a,21-dihydroxiprogesteron
DHA = dehydroepiandrosteron
DHAS = dehydroepiandro-steronsulfat

Enzym: 3ßHSD = 3ß-hydroxisteroidoxidoreduktas (”3ß-oldehydrogenas”)
18HSD = 18-hydroxisteroidoxidoreduktas
11OH = 11ß-hydroxylas
17OH = 17a-hydroxylas
18OH = 18-hydroxylas
21OH = 21-hydroxylas.